full name
acyl-CoA dehydrogenase, very long chain

synonyms
ACAD6, LCACD, VLCAD, ACADVL, ENSG00000072778

HGNC
HGNC:92

Entrez Gene
Gene:37

ENSEMBL
ENSG00000072778

location
chr: 17
start: 7120444
stop: 7128586
strand: +

OMIM
OMIM:609575: ACADVL (Autosomal recessive inheritance)
OMIM:201475: VLCAD deficiency

transcripts
NM_001270447.1
NM_001270448.1
NM_000018.3
NM_001033859.2

pathways
Beta oxidation of palmitoyl-CoA to myristoyl-CoA [NCBI:1270017] [REACTOME:R-HSA-77305]
FOXA2 and FOXA3 transcription factor networks [NCBI:137911] [Pathway Interaction Database:hnf3bpathway] [PUBMED:2786140] [PUBMED:9632808] [PUBMED:10748140] [PUBMED:8662915] [PUBMED:12865419] [PUBMED:15123725] [PUBMED:15314688] [PUBMED:12145169] [PUBMED:16098831] [PUBMED:10455192] [PUBMED:15616563] [PUBMED:7524494] [PUBMED:7565696] [PUBMED:15959514] [PUBMED:8813720] [PUBMED:11278466] [PUBMED:9369482] [PUBMED:14500912] [PUBMED:8668179] [PUBMED:12911579]
Fatty Acid Beta Oxidation [NCBI:198865] [WikiPathways:WP143]
Fatty acid degradation [NCBI:82935] [KEGG:hsa00071] [PUBMED:869535]
Fatty acid metabolism [NCBI:868084] [KEGG:hsa01212]
Fatty acid, triacylglycerol, and ketone body metabolism [NCBI:1270010] [REACTOME:R-HSA-535734]
IRE1alpha activates chaperones [NCBI:1268759] [REACTOME:R-HSA-381070] [PUBMED:18038217] [PUBMED:18436705] [PUBMED:18048764]
Metabolic pathways [NCBI:132956] [KEGG:hsa01100]
Metabolism [NCBI:1269956] [REACTOME:R-HSA-1430728]
Metabolism of lipids and lipoproteins [NCBI:1270001] [REACTOME:R-HSA-556833]
Metabolism of proteins [NCBI:1268677] [REACTOME:R-HSA-392499]
Mitochondrial Fatty Acid Beta-Oxidation [NCBI:1270015] [REACTOME:R-HSA-77289] [PUBMED:10527676] [PUBMED:11826276] [PUBMED:7951672] [PUBMED:1431593]
Mitochondrial LC-Fatty Acid Beta-Oxidation [NCBI:198817] [WikiPathways:WP368]
Unfolded Protein Response (UPR) [NCBI:1268756] [REACTOME:R-HSA-381119] [PUBMED:18436705] [PUBMED:18038217] [PUBMED:16365312] [PUBMED:15952902] [PUBMED:18048764]
XBP1(S) activates chaperone genes [NCBI:1268760] [REACTOME:R-HSA-381038] [PUBMED:16461360] [PUBMED:14559994] [PUBMED:18664523] [PUBMED:16539657] [PUBMED:17612490]
beta-Oxidation [NCBI:413381] [KEGG:hsa_M00087]
mitochondrial fatty acid beta-oxidation of saturated fatty acids [NCBI:1270016] [REACTOME:R-HSA-77286]